The following table is a corrected version of the one appearing in Devlin on p. 349.
| Disease | Deficient Enzymeb |
|---|---|
| Aspartylglycosylaminuria | 4-L-Aspartylglycosylamine amidohydrolase (a) |
| b-Mannosidosis | b-Mannosidase (7) |
| a-Mannosidosis | a-Mannosidase (3) |
| GM2
Gangliosidosis variant O (Sandhoff-Jatzkewitz disease) |
b-N-Acetylhexosaminidases (A and B) (4) |
| GM1 Gangliosidosis | b-Galactosidase (5) |
| Mucolipidosis I (Sialidosis) | Sialidase (6) |
| Fucosidosis | a-Fucosidase (8) |
|
a A typical Asn-GlcNAc oligosaccharide structure:  |
|
| b The numbers in parentheses refer to the enzymes that hydrolyze those bonds. | |
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