The following table is a corrected version of the one appearing in Devlin on p. 352.
| Disease | Accumulated Products | Deficient Enzymeb |
|---|---|---|
| Hunter | Heparan
sulfate Dermatan sulfate |
Iduronate sulfatase (1) |
| Hurler + Scheie | Heparan
sulfate Dermatan sulfate |
a-L-Iduronidase (2) |
| Maroteaux-Lamy | Dermatan sulfate | N-Acetylgalactosamine sulfatase(3) |
| Mucolipidosis VII | Heparan
sulfate Dermatan sulfate |
b-Glucuronidase (5) |
| Sanfilippo A | Heparan sulfate | Heparan sulfamidase (6) |
| Sanfilippo B | Heparan sulfate | N-Acetylglucosaminidase (9) |
| Sanfilippo D | Heparan sulfate | N-Acetylglucosamine-6-sulfatase (8) |
|
a Structures of dermatan sulfate and heparan sulfate:  |
||
| b The numbers in parentheses refer to the enzymes that hydrolyze those bonds. | ||
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